Acute idiopathic blind spot enlargement syndrome

Acute idiopathic blind spot enlargement syndrome (AIBSE) is a rare eye disease affecting the retina of the eye. It is basically a type of retinopathy which affects females more than males. Currently there is no treatment for this condition, but, it is usually self limiting.

Acute idiopathic blind spot enlargement syndrome
Other namesAIBSE syndrome
SpecialtyOphthalmology
Diagnostic methodEye examination, Visual field test
TreatmentNil, Usually self limiting

Cause

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Though exact etiology of AIBSE syndrome is unknown, studies shows that viral illness like influenza and vaccinations like MMR may trigger the condition.[1]

Demographics

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AIBSE syndrome affects females more than males.[1] Higher incidence is seen in Caucasian people.[1]

Signs and Symptoms

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Enlargement of blind spot area in the visual field of the eye is the main sign and acute onset photopsia is the main symptom of AIBSE syndrome.[2] Other symptoms include monocular scotoma and reduced light perception.[3]

Diagnosis

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Diagnostic techniques like ophthalmoscopy, visual field test, optical coherence tomography, fluorescein angiography, multifocal electroretinography and electrophysiology may be used in diagnosing AIBSE syndrome.[2] Subjective measurement of blind spot enlargement is done using visual field testing.[4] In the early stages, using FFA peripapillary hyperfluorescence may be observed.[4] Since OCT can be used to observe the microstructural alterations in the outer retina, it is the gold standard in diagnosing AIBSES.[2]

Treatment

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Currently there is no treatment for this condition, but, it is usually self limiting.[1] Systemic administration of corticosteroids may be advised.[2] Even if the disease is resolved, the enlarged blind spot usually does not return to normal.[5]

History

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Fletcher et al. first described AIBSE syndrome in 1988.[2]

Reference

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  1. ^ a b c d "Acute Idiopathic Blind Spot Enlargement (AIBSE) Syndrome - EyeWiki". eyewiki.aao.org.
  2. ^ a b c d e Zimmermann, Julian A.; Eter, Nicole; Biermann, Julia (7 September 2022). "Acute Idiopathic Blind Spot Enlargement Syndrome—New Perspectives in the OCT Era". Journal of Clinical Medicine. 11 (18): 5278. doi:10.3390/jcm11185278. ISSN 2077-0383. PMC 9501978. PMID 36142923.
  3. ^ Wong, Melody; Campos-Baniak, Maria Gabriela; Colleaux, Kevin (August 2019). "Acute idiopathic blind spot enlargement syndrome following measles, mumps and rubella vaccination". Canadian Journal of Ophthalmology. 54 (4): e199–e203. doi:10.1016/j.jcjo.2018.09.005. PMID 31358170.
  4. ^ a b Ishihara, Rhys; Khan, Youan; Halim, Muhammad Sohail; Akhavanrezayat, Amir; Onghanseng, Neil; Levin, Marc Harris; Nguyen, Quan Dong (March 2023). "Acute idiopathic blind spot enlargement syndrome (AIBSES) with retinal vasculitis". American Journal of Ophthalmology Case Reports. 29: 101760. doi:10.1016/j.ajoc.2022.101760. ISSN 2451-9936. PMC 9763352. PMID 36561880.
  5. ^ "The Case of the Enormous Blind Spot". Retina Today.